Abstract
Dandy Walker malformation (DWM) is a rare congenital brain anomaly characterized by cystic dilation of the fourth ventricle and hypoplasia of the cerebellar vermis. Other extracranial anomalies can be associated, including cardiac defects. We report a rare patient with DWM associated with progressive heart failure secondary to hypertrophic cardiomyopathy. He was diagnosed at 2 months of age and died 5 months later. We conclude that hypertrophic cardiomyopathy can be associated with DWM with poor prognosis. A careful cardiac evaluation is needed in all infants with DWM for early recognition of such potentially serious associated cardiac malformations.
Article Type
Case Report
First Page
368
Last Page
370
Recommended Citation
Kurdi, Maher E.; Chamsi-Pasha, Mohammed A.; Baeesa, Saleh S.; and Jan, Mohammed M.
(2009)
"Dandy Walker malformation and hypertrophic cardiomyopathy. Unusual fatal association,"
Neurosciences: Vol. 14:
Iss.
4, Article 10.
DOI: https://doi.org/10.17712/1658-3183.1744